Lymphoscintigraphy patterns in newborns and children with congenital lymphatic dysplasia.
Identifieur interne : 002870 ( Main/Exploration ); précédent : 002869; suivant : 002871Lymphoscintigraphy patterns in newborns and children with congenital lymphatic dysplasia.
Auteurs : C. Bellini ; G. Villa ; G. Sambuceti ; C. Traggiai ; C. Campisi ; T. Bellini ; G. Morcaldi ; D. Massocco ; E. Bonioli ; F. BoccardoSource :
- Lymphology [ 0024-7766 ] ; 2014.
Descripteurs français
- KwdFr :
- Anasarque foeto-placentaire (imagerie diagnostique), Ascite chyleuse (imagerie diagnostique), Chylothorax (), Chylothorax (imagerie diagnostique), Enfant, Enfant d'âge préscolaire, Humains, Indice de gravité médicale, Lymphangiectasie (), Lymphangiectasie (imagerie diagnostique), Lymphangiectasie intestinale (imagerie diagnostique), Lymphoedème (imagerie diagnostique), Lymphoscintigraphie, Maladies lymphatiques (), Maladies lymphatiques (imagerie diagnostique), Maladies pulmonaires (), Maladies pulmonaires (imagerie diagnostique), Nourrisson, Nouveau-né, Pronostic, Système lymphatique (malformations), Valeur prédictive des tests, Épanchement péricardique (imagerie diagnostique).
- MESH :
- imagerie diagnostique : Anasarque foeto-placentaire, Ascite chyleuse, Chylothorax, Lymphangiectasie, Lymphangiectasie intestinale, Lymphoedème, Maladies lymphatiques, Maladies pulmonaires, Épanchement péricardique.
- malformations : Système lymphatique.
- Chylothorax, Enfant, Enfant d'âge préscolaire, Humains, Indice de gravité médicale, Lymphangiectasie, Lymphoscintigraphie, Maladies lymphatiques, Maladies pulmonaires, Nourrisson, Nouveau-né, Pronostic, Valeur prédictive des tests.
English descriptors
- KwdEn :
- Child, Child, Preschool, Chylothorax (congenital), Chylothorax (diagnostic imaging), Chylous Ascites (diagnostic imaging), Humans, Hydrops Fetalis (diagnostic imaging), Infant, Infant, Newborn, Lung Diseases (congenital), Lung Diseases (diagnostic imaging), Lymphangiectasis (congenital), Lymphangiectasis (diagnostic imaging), Lymphangiectasis, Intestinal (diagnostic imaging), Lymphatic Diseases (congenital), Lymphatic Diseases (diagnostic imaging), Lymphatic Diseases (therapy), Lymphatic System (abnormalities), Lymphedema (diagnostic imaging), Lymphoscintigraphy, Pericardial Effusion (diagnostic imaging), Predictive Value of Tests, Prognosis, Severity of Illness Index.
- MESH :
- abnormalities : Lymphatic System.
- congenital : Chylothorax, Lung Diseases, Lymphangiectasis, Lymphatic Diseases.
- diagnostic imaging : Chylothorax, Chylous Ascites, Hydrops Fetalis, Lung Diseases, Lymphangiectasis, Lymphangiectasis, Intestinal, Lymphatic Diseases, Lymphedema, Pericardial Effusion.
- therapy : Lymphatic Diseases.
- Child, Child, Preschool, Humans, Infant, Infant, Newborn, Lymphoscintigraphy, Predictive Value of Tests, Prognosis, Severity of Illness Index.
Abstract
We performed lymphoscintigraphy on 31 patients (newborns and children) affected by congenital lymphatic dysplasia according to our previously published protocol. Congenital lymphatic dysplasia may present with various degrees of clinical severity, ranging from nonimmune hydrops fetalis with visceral effusions to lymphedema alone. We recommend that lymphoscintigraphy should be strongly considered in all patients with signs of lymphatic dysplasia, including those with minimal and initial signs of lymphatic impairment, in order to obtain a very early diagnosis and to start treatment. Lymphoscintigraphy is safe and useful in the diagnosis of lymphatic dysplasia in the newborn and children. Moreover, it is well tolerated by patients and well accepted by their parents.
PubMed: 25109167
Affiliations:
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Le document en format XML
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<author><name sortKey="Bellini, C" sort="Bellini, C" uniqKey="Bellini C" first="C" last="Bellini">C. Bellini</name>
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<author><name sortKey="Villa, G" sort="Villa, G" uniqKey="Villa G" first="G" last="Villa">G. Villa</name>
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<author><name sortKey="Sambuceti, G" sort="Sambuceti, G" uniqKey="Sambuceti G" first="G" last="Sambuceti">G. Sambuceti</name>
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<series><title level="j">Lymphology</title>
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Child</term>
<term>Child, Preschool</term>
<term>Chylothorax (congenital)</term>
<term>Chylothorax (diagnostic imaging)</term>
<term>Chylous Ascites (diagnostic imaging)</term>
<term>Humans</term>
<term>Hydrops Fetalis (diagnostic imaging)</term>
<term>Infant</term>
<term>Infant, Newborn</term>
<term>Lung Diseases (congenital)</term>
<term>Lung Diseases (diagnostic imaging)</term>
<term>Lymphangiectasis (congenital)</term>
<term>Lymphangiectasis (diagnostic imaging)</term>
<term>Lymphangiectasis, Intestinal (diagnostic imaging)</term>
<term>Lymphatic Diseases (congenital)</term>
<term>Lymphatic Diseases (diagnostic imaging)</term>
<term>Lymphatic Diseases (therapy)</term>
<term>Lymphatic System (abnormalities)</term>
<term>Lymphedema (diagnostic imaging)</term>
<term>Lymphoscintigraphy</term>
<term>Pericardial Effusion (diagnostic imaging)</term>
<term>Predictive Value of Tests</term>
<term>Prognosis</term>
<term>Severity of Illness Index</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr"><term>Anasarque foeto-placentaire (imagerie diagnostique)</term>
<term>Ascite chyleuse (imagerie diagnostique)</term>
<term>Chylothorax ()</term>
<term>Chylothorax (imagerie diagnostique)</term>
<term>Enfant</term>
<term>Enfant d'âge préscolaire</term>
<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Lymphangiectasie ()</term>
<term>Lymphangiectasie (imagerie diagnostique)</term>
<term>Lymphangiectasie intestinale (imagerie diagnostique)</term>
<term>Lymphoedème (imagerie diagnostique)</term>
<term>Lymphoscintigraphie</term>
<term>Maladies lymphatiques ()</term>
<term>Maladies lymphatiques (imagerie diagnostique)</term>
<term>Maladies pulmonaires ()</term>
<term>Maladies pulmonaires (imagerie diagnostique)</term>
<term>Nourrisson</term>
<term>Nouveau-né</term>
<term>Pronostic</term>
<term>Système lymphatique (malformations)</term>
<term>Valeur prédictive des tests</term>
<term>Épanchement péricardique (imagerie diagnostique)</term>
</keywords>
<keywords scheme="MESH" qualifier="abnormalities" xml:lang="en"><term>Lymphatic System</term>
</keywords>
<keywords scheme="MESH" qualifier="congenital" xml:lang="en"><term>Chylothorax</term>
<term>Lung Diseases</term>
<term>Lymphangiectasis</term>
<term>Lymphatic Diseases</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic imaging" xml:lang="en"><term>Chylothorax</term>
<term>Chylous Ascites</term>
<term>Hydrops Fetalis</term>
<term>Lung Diseases</term>
<term>Lymphangiectasis</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphatic Diseases</term>
<term>Lymphedema</term>
<term>Pericardial Effusion</term>
</keywords>
<keywords scheme="MESH" qualifier="imagerie diagnostique" xml:lang="fr"><term>Anasarque foeto-placentaire</term>
<term>Ascite chyleuse</term>
<term>Chylothorax</term>
<term>Lymphangiectasie</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
<term>Maladies lymphatiques</term>
<term>Maladies pulmonaires</term>
<term>Épanchement péricardique</term>
</keywords>
<keywords scheme="MESH" qualifier="malformations" xml:lang="fr"><term>Système lymphatique</term>
</keywords>
<keywords scheme="MESH" qualifier="therapy" xml:lang="en"><term>Lymphatic Diseases</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Child</term>
<term>Child, Preschool</term>
<term>Humans</term>
<term>Infant</term>
<term>Infant, Newborn</term>
<term>Lymphoscintigraphy</term>
<term>Predictive Value of Tests</term>
<term>Prognosis</term>
<term>Severity of Illness Index</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr"><term>Chylothorax</term>
<term>Enfant</term>
<term>Enfant d'âge préscolaire</term>
<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Lymphangiectasie</term>
<term>Lymphoscintigraphie</term>
<term>Maladies lymphatiques</term>
<term>Maladies pulmonaires</term>
<term>Nourrisson</term>
<term>Nouveau-né</term>
<term>Pronostic</term>
<term>Valeur prédictive des tests</term>
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<front><div type="abstract" xml:lang="en">We performed lymphoscintigraphy on 31 patients (newborns and children) affected by congenital lymphatic dysplasia according to our previously published protocol. Congenital lymphatic dysplasia may present with various degrees of clinical severity, ranging from nonimmune hydrops fetalis with visceral effusions to lymphedema alone. We recommend that lymphoscintigraphy should be strongly considered in all patients with signs of lymphatic dysplasia, including those with minimal and initial signs of lymphatic impairment, in order to obtain a very early diagnosis and to start treatment. Lymphoscintigraphy is safe and useful in the diagnosis of lymphatic dysplasia in the newborn and children. Moreover, it is well tolerated by patients and well accepted by their parents.</div>
</front>
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<affiliations><list></list>
<tree><noCountry><name sortKey="Bellini, C" sort="Bellini, C" uniqKey="Bellini C" first="C" last="Bellini">C. Bellini</name>
<name sortKey="Bellini, T" sort="Bellini, T" uniqKey="Bellini T" first="T" last="Bellini">T. Bellini</name>
<name sortKey="Boccardo, F" sort="Boccardo, F" uniqKey="Boccardo F" first="F" last="Boccardo">F. Boccardo</name>
<name sortKey="Bonioli, E" sort="Bonioli, E" uniqKey="Bonioli E" first="E" last="Bonioli">E. Bonioli</name>
<name sortKey="Campisi, C" sort="Campisi, C" uniqKey="Campisi C" first="C" last="Campisi">C. Campisi</name>
<name sortKey="Massocco, D" sort="Massocco, D" uniqKey="Massocco D" first="D" last="Massocco">D. Massocco</name>
<name sortKey="Morcaldi, G" sort="Morcaldi, G" uniqKey="Morcaldi G" first="G" last="Morcaldi">G. Morcaldi</name>
<name sortKey="Sambuceti, G" sort="Sambuceti, G" uniqKey="Sambuceti G" first="G" last="Sambuceti">G. Sambuceti</name>
<name sortKey="Traggiai, C" sort="Traggiai, C" uniqKey="Traggiai C" first="C" last="Traggiai">C. Traggiai</name>
<name sortKey="Villa, G" sort="Villa, G" uniqKey="Villa G" first="G" last="Villa">G. Villa</name>
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