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Lymphoscintigraphy patterns in newborns and children with congenital lymphatic dysplasia.

Identifieur interne : 002870 ( Main/Exploration ); précédent : 002869; suivant : 002871

Lymphoscintigraphy patterns in newborns and children with congenital lymphatic dysplasia.

Auteurs : C. Bellini ; G. Villa ; G. Sambuceti ; C. Traggiai ; C. Campisi ; T. Bellini ; G. Morcaldi ; D. Massocco ; E. Bonioli ; F. Boccardo

Source :

RBID : pubmed:25109167

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English descriptors

Abstract

We performed lymphoscintigraphy on 31 patients (newborns and children) affected by congenital lymphatic dysplasia according to our previously published protocol. Congenital lymphatic dysplasia may present with various degrees of clinical severity, ranging from nonimmune hydrops fetalis with visceral effusions to lymphedema alone. We recommend that lymphoscintigraphy should be strongly considered in all patients with signs of lymphatic dysplasia, including those with minimal and initial signs of lymphatic impairment, in order to obtain a very early diagnosis and to start treatment. Lymphoscintigraphy is safe and useful in the diagnosis of lymphatic dysplasia in the newborn and children. Moreover, it is well tolerated by patients and well accepted by their parents.

PubMed: 25109167


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Le document en format XML

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<term>Chylothorax (diagnostic imaging)</term>
<term>Chylous Ascites (diagnostic imaging)</term>
<term>Humans</term>
<term>Hydrops Fetalis (diagnostic imaging)</term>
<term>Infant</term>
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<term>Lung Diseases (congenital)</term>
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<term>Lymphatic System (abnormalities)</term>
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<term>Lymphoscintigraphy</term>
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<term>Predictive Value of Tests</term>
<term>Prognosis</term>
<term>Severity of Illness Index</term>
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<term>Ascite chyleuse (imagerie diagnostique)</term>
<term>Chylothorax ()</term>
<term>Chylothorax (imagerie diagnostique)</term>
<term>Enfant</term>
<term>Enfant d'âge préscolaire</term>
<term>Humains</term>
<term>Indice de gravité médicale</term>
<term>Lymphangiectasie ()</term>
<term>Lymphangiectasie (imagerie diagnostique)</term>
<term>Lymphangiectasie intestinale (imagerie diagnostique)</term>
<term>Lymphoedème (imagerie diagnostique)</term>
<term>Lymphoscintigraphie</term>
<term>Maladies lymphatiques ()</term>
<term>Maladies lymphatiques (imagerie diagnostique)</term>
<term>Maladies pulmonaires ()</term>
<term>Maladies pulmonaires (imagerie diagnostique)</term>
<term>Nourrisson</term>
<term>Nouveau-né</term>
<term>Pronostic</term>
<term>Système lymphatique (malformations)</term>
<term>Valeur prédictive des tests</term>
<term>Épanchement péricardique (imagerie diagnostique)</term>
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<term>Indice de gravité médicale</term>
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<term>Lymphoscintigraphie</term>
<term>Maladies lymphatiques</term>
<term>Maladies pulmonaires</term>
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<front>
<div type="abstract" xml:lang="en">We performed lymphoscintigraphy on 31 patients (newborns and children) affected by congenital lymphatic dysplasia according to our previously published protocol. Congenital lymphatic dysplasia may present with various degrees of clinical severity, ranging from nonimmune hydrops fetalis with visceral effusions to lymphedema alone. We recommend that lymphoscintigraphy should be strongly considered in all patients with signs of lymphatic dysplasia, including those with minimal and initial signs of lymphatic impairment, in order to obtain a very early diagnosis and to start treatment. Lymphoscintigraphy is safe and useful in the diagnosis of lymphatic dysplasia in the newborn and children. Moreover, it is well tolerated by patients and well accepted by their parents.</div>
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<name sortKey="Bellini, C" sort="Bellini, C" uniqKey="Bellini C" first="C" last="Bellini">C. Bellini</name>
<name sortKey="Bellini, T" sort="Bellini, T" uniqKey="Bellini T" first="T" last="Bellini">T. Bellini</name>
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<name sortKey="Campisi, C" sort="Campisi, C" uniqKey="Campisi C" first="C" last="Campisi">C. Campisi</name>
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